Ebstein's anomaly


Our cardiology experts can help to treat you or your child if you or they have Ebstein's anomaly

Enquiries & Appointments

Female pediatrician listens to young patient's heartbeat 637014216.jpg

About Ebstein's anomaly

Ebstein's anomaly is when the tricuspid valve on the right side of the heart does not work properly. Blood may then flow the wrong way in the heart. This can occur along with an atrial septal defect (hole in the heart). A range of treatments are available. In some cases, valve repair or replacement surgery may be recommended by your consultant.

Need to know

In babies:

  • cyanosis (bluish discoloration of the skin)
  • shortness of breath

Older children and adults:

  • shortness of breath
  • fatigue during play
  • heart palpitations/irregular heartbeat (arrhythmia)
  • cyanosis
  • leg swelling

Your child's consultant will your discuss symptoms with you. The following tests can be carried out if they suspect you or your child may have Ebstein's anomaly:

  • chest X-ray to determine if you or your child has an enlarged hear
  • an echocardiogram to monitor any heart defects through ultrasonic waves
  • an electrocardiogram (ECG) uses sensors (electrodes) to assess heartbeat regularity
  • Holter monitor (essentially a portable ECG) to be worn for one to two days
  • cardiac catheterisation is a less common technique to assess blood flow through the heart and vessels

Your consultant will discuss treatment options and the best possible approach for you or your child. These might include:

  • monitoring through physical examinations
  • medication to control heart rate and rhythm
  • surgery may be required to either repair or replace the tricuspid valve
  • If Ebstein's anomaly occurs along with atrial septal defect, the hole can be closed at the same time

Our locations

The Harley Street Clinic

The Harley Street Clinic

35 Weymouth Street W1G 8BJ London
The Lister Hospital

The Lister Hospital

Chelsea Bridge Road, SW1W 8RH London
The Cardiac Clinic

The Cardiac Clinic

London Bridge Hospital SE1 2PR London

Patient stories

This content is intended for general information only and does not replace the need for personal advice from a qualified health professional.