Ebstein's anomaly

Rare heart defect

Our cardiology experts can help to treat you or your child if you or they have Ebstein's anomaly

About Ebstein's anomaly

Ebstein's anomaly is when the tricuspid valve on the right side of the heart does not work properly. Blood may then flow the wrong way in the heart. This can occur along with an atrial septal defect (hole in the heart). A range of treatments are available. In some cases, valve repair or replacement surgery may be recommended by your consultant.

Need to know

  • What are the symptoms of Ebstein's anomaly? icon plus

    In babies:

    • cyanosis (bluish discoloration of the skin)
    • shortness of breath

    Older children and adults:

    • shortness of breath
    • fatigue during play
    • heart palpitations/irregular heartbeat (arrhythmia)
    • cyanosis
    • leg swelling
  • Diagnosing Ebsteins anomaly icon plus

    Your child's consultant will your discuss symptoms with you. The following tests can be carried out if they suspect you or your child may have Ebstein's anomaly:

    • chest X-ray to determine if you or your child has an enlarged hear
    • an echocardiogram to monitor any heart defects through ultrasonic waves
    • an electrocardiogram (ECG) uses sensors (electrodes) to assess heartbeat regularity
    • Holter monitor (essentially a portable ECG) to be worn for one to two days
    • cardiac catheterisation is a less common technique to assess blood flow through the heart and vessels
  • Potential treatment options icon plus

    Your consultant will discuss treatment options and the best possible approach for you or your child. These might include:

    • monitoring through physical examinations
    • medication to control heart rate and rhythm
    • surgery may be required to either repair or replace the tricuspid valve
    • If Ebstein's anomaly occurs along with atrial septal defect, the hole can be closed at the same time

Our cardiologists

We're proud to work with leading cardiac experts including cardiothoracic surgeons and physiologists whose skills are matched by their integrity and compassion.
Consultant in theatres

Our locations

From complex cardiothoracic surgery to diagnostic tests and procedures, we provide exceptional cardiac care across our network of hospitals, outpatient centres and specialist clinics.

Request an appointment

Our team can help with any enquiries or you make an appointment with one of our experienced consultants.

Call us today

020 7079 4344
This content is intended for general information only and does not replace the need for personal advice from a qualified health professional.
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